No abstract available
MeSH terms
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Adenosine Triphosphatases / genetics
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Adenosine Triphosphatases / metabolism
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Adenosine Triphosphate / metabolism*
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Animals
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Biological Assay / methods
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Cells, Cultured
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DNA, Mitochondrial / genetics
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DNA, Mitochondrial / metabolism
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Digitonin / pharmacology
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Fibroblasts / drug effects
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Fibroblasts / metabolism
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Firefly Luciferin / metabolism
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Humans
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Indicators and Reagents / pharmacology
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Leigh Disease / metabolism
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Luciferases / metabolism
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Luminescent Measurements
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Mitochondria / drug effects
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Mitochondria / enzymology
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Mitochondria / metabolism*
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Mitochondrial Diseases / metabolism
Substances
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DNA, Mitochondrial
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Indicators and Reagents
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Firefly Luciferin
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Adenosine Triphosphate
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Luciferases
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Adenosine Triphosphatases
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Digitonin