Rapidly progressive bilateral sensory neural hearing loss as a presentation of mitochondrial neurogastrointestinal encephalomyopathy

Am J Otolaryngol. 2003 Mar-Apr;24(2):128-30. doi: 10.1053/ajot.2003.25.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Audiometry, Pure-Tone
  • Diagnosis, Differential
  • Disease Progression
  • Female
  • Follow-Up Studies
  • Hearing Loss, Bilateral / diagnosis
  • Hearing Loss, Bilateral / etiology
  • Hearing Loss, Sensorineural / diagnosis
  • Hearing Loss, Sensorineural / etiology*
  • Humans
  • Magnetic Resonance Imaging / methods
  • Mitochondrial Encephalomyopathies / complications*
  • Mitochondrial Encephalomyopathies / diagnosis*
  • Risk Assessment
  • Severity of Illness Index