Severe acute necrotizing pancreatitis associated with lipoprotein lipase deficiency in childhood

J Pediatr Surg. 2003 Sep;38(9):1407-8. doi: 10.1016/s0022-3468(03)00409-3.

Abstract

An 11-year-old girl with lipoprotein lipase deficiency experienced recurring episodes of abdominal pain. She initially underwent appendectomy for suspected appendicitis; however, the appendix was normal. Pancreatitis was subsequently identified as the cause of her pain.

Publication types

  • Case Reports

MeSH terms

  • Abdomen, Acute / etiology
  • Amylases / blood
  • Appendicitis / diagnosis*
  • Child
  • Diagnostic Errors
  • Female
  • Humans
  • Hyperlipoproteinemia Type I / complications*
  • Hyperlipoproteinemia Type I / metabolism
  • Lipase / blood
  • Pancreatitis, Acute Necrotizing / diagnosis*
  • Pancreatitis, Acute Necrotizing / etiology*
  • Pancreatitis, Acute Necrotizing / metabolism

Substances

  • Lipase
  • Amylases