A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis

Gabrielle H van Ramshorst; Maarten H Lequin; Grazia M S Mancini; Cornelis P van de Ven

doi:10.1016/j.jpedsurg.2006.09.070

A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis

J Pediatr Surg. 2006 Dec;41(12):e19-23. doi: 10.1016/j.jpedsurg.2006.09.070.

Authors

Gabrielle H van Ramshorst¹, Maarten H Lequin, Grazia M S Mancini, Cornelis P van de Ven

Affiliation

¹ Department of Pediatric Surgery, Erasmus Medical Center/Sophia Children's Hospital, 3000 CB Rotterdam, the Netherlands.

PMID: 17161173
DOI: 10.1016/j.jpedsurg.2006.09.070

Abstract

The authors describe a case of split notochord syndrome with a neuroenteric fistula in a newborn presenting with meningitis. Associated anomalies included agenesis of the corpus callosum, short colon, malrotation, epispadias, and an abnormally high bifurcation of the abdominal aorta and inferior vena cava. The embryological mechanisms and etiologic theories are discussed in short.

Publication types

Case Reports

MeSH terms

Abnormalities, Multiple*
Central Nervous System Diseases / complications
Central Nervous System Diseases / diagnosis*
Central Nervous System Diseases / surgery
Colonic Diseases / complications
Colonic Diseases / diagnosis*
Colonic Diseases / surgery
Humans
Infant, Newborn
Intestinal Fistula / complications
Intestinal Fistula / diagnosis*
Intestinal Fistula / surgery
Male
Meningitis / etiology*
Notochord / abnormalities*
Syndrome