The dystrophinopathies in Costa Rica

Rev Biol Trop. 2004 Sep;52(3):485-90. doi: 10.15517/rbt.v1i2.15286.

Abstract

A five-years long study aiming to describe the basic genetic epidemiology of the dystrophinopathies in Costa Rica recruited 31 patients with clinical symptoms of DMD/BMD at the National Children's Hospital (HNN). This center is the obligate reference hospital of the national health system for genetic diseases, however, the geographic origin of the patients, a low percentage of deletions and a high proportion of de novo mutations found among them indicate that a significant ascertainment bias impedes a substantial scientific approach to confront and alleviate the problems posed by these severe diseases in Costa Rica.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Chromosomes, Human, X / genetics
  • Costa Rica
  • Female
  • Genetic Carrier Screening*
  • Genetic Linkage
  • Genetic Markers
  • Humans
  • Male
  • Muscular Dystrophy, Duchenne / genetics*
  • Mutation / genetics*
  • Polymerase Chain Reaction

Substances

  • Genetic Markers