Primary neuroectodermal tumor of penis (PNET)--a case report

Urology. 2007 Oct;70(4):811.e9-10. doi: 10.1016/j.urology.2007.07.031.

Abstract

Primary neuroectodermal tumor (PNET) is a rare entity with high malignant potential. It usually affects the skeletal system and primary extraskeletal involvement is uncommon. Because of rarity of tumor in the penis, only a few cases have been reported. A 17-year-old male adolescent presented with painless penile swelling of 4 weeks' duration. Clinical examination revealed multiple, 1 cm hard nodules palpable on penile shaft. Open incisional biopsy of the penile nodule revealed an undifferentiated malignant round cell tumor and on immunohistochemistry a diagnosis of PNET was made. Metastatic workup was negative. Total penectomy and perineal urethrostomy was performed, and subsequently adjuvant chemotherapy was given.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Humans
  • Male
  • Neuroectodermal Tumors, Primitive* / diagnosis
  • Neuroectodermal Tumors, Primitive* / surgery
  • Penile Neoplasms* / diagnosis
  • Penile Neoplasms* / surgery
  • Penis / surgery