[New therapeutic approaches in mitochondrial fatty acid oxidation disorders]

Arch Pediatr. 2008 Jun;15(5):608-10. doi: 10.1016/S0929-693X(08)71849-9.
[Article in French]
No abstract available

MeSH terms

  • Carnitine / analogs & derivatives
  • Carnitine / metabolism
  • Citric Acid Cycle
  • Fatty Acids / metabolism
  • Humans
  • Mitochondrial Diseases / therapy*
  • Mitochondrial Trifunctional Protein
  • Multienzyme Complexes / metabolism*

Substances

  • Fatty Acids
  • Multienzyme Complexes
  • acylcarnitine
  • Mitochondrial Trifunctional Protein
  • Carnitine