4.3-Mb triplication of 4q32.1-q32.2: report of a family through two generations

Am J Med Genet A. 2009 Oct;149A(10):2274-9. doi: 10.1002/ajmg.a.33020.

Abstract

Duplications of 4q31-qter have been rarely documented; moreover, triplications at this chromosomal region have never been described. Here we report a family through two generations (mother and three sons) with triplication of 4q32.1-q32.2. Their characteristic features include: macrocephaly, a long midface, hypoplastic zygoma, wide nasal bridge, short nose, downslanting and small palpebral fissures, and small, low-set and squared-off ears. Among the three sons, two had Hirschsprung disease, and one had constipation at birth. The phenotype of triplication of 4q32.1-q32.2 appeared to be distinct from duplications of 4q31-qter.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Child
  • Child Development Disorders, Pervasive / complications
  • Child Development Disorders, Pervasive / genetics
  • Child, Preschool
  • Chromosome Aberrations*
  • Chromosomes, Human, Pair 4*
  • Craniofacial Abnormalities / complications
  • Craniofacial Abnormalities / genetics
  • Family Characteristics
  • Family*
  • Female
  • Gene Duplication*
  • Humans
  • Intellectual Disability / complications
  • Intellectual Disability / genetics
  • Male