Vascular abnormalities in epidermal nevus syndrome

Neurology. 1991 Feb;41(2 ( Pt 1)):276-8. doi: 10.1212/wnl.41.2_part_1.276.

Abstract

We report a patient with epidermal nevus syndrome and right hemispheric infarct and review 3 others with neurologic manifestations best explained by ischemia or hemorrhage. Each had a significant vascular abnormality such as occlusion or blood vessel dysplasia. None had hemimegalencephaly. We hypothesize that underlying vascular dysplasia is the cause of the neurologic lesions in these patients.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Cerebral Infarction / complications
  • Cerebral Infarction / diagnostic imaging
  • Child
  • Child, Preschool
  • Humans
  • Male
  • Nevus, Pigmented / complications*
  • Scalp
  • Skin Neoplasms / complications*
  • Syndrome
  • Tomography, X-Ray Computed
  • Vascular Diseases / complications*