Clinical and functional outcome and factors predicting prognosis in osmotic demyelination syndrome (central pontine and/or extrapontine myelinolysis) in 25 patients

J Neurol Neurosurg Psychiatry. 2011 Mar;82(3):326-31. doi: 10.1136/jnnp.2009.201764. Epub 2010 Sep 8.

Abstract

Aims: To assess the functional and clinical outcome in a sizeable cohort of patients with osmotic demyelination syndrome (ODS) and to characterise the factors which could predict the final outcome.

Methods: Twenty five consecutive patients with ODS formed the study cohort. The diagnosis of ODS was based on clinical features with corroborating imaging findings. Two functional scales--Functional Independent Measure (FIM) and Disability Rating Scale (DRS)--were applied to assess the functional status at the time of admission, discharge and last follow-up. Patients who became independent for activities of daily living (ADL) at last follow-up were classified as favourable outcome, and those who died or became dependent for ADL were classified as a poor outcome group respectively. The Fisher exact test and Mann-Whitney U test were used to assess categorical and continuous variables respectively.

Results: The mean age at diagnosis was 53 ± 14 years. Five (20%) had central pontine myelinolysis, seven (28%) had extrapontine myelinolysis, and 13 (52%) had both. Hyponatraemia and hypokalaemia were noted in 20 (80%) and 10 (40%) patients respectively. Six (24%) received intravenous methylprednisolone. Eleven (46%) had a favourable outcome at a mean follow-up of 2.2 ± 2.5 years. Hyponatraemia ≤ 115 mEq (p=0.04), associated hypokalaemia (p=0.04) and low Glasgow Coma Scale (GCS) (p=0.008) at presentation were predictive of poor outcome. The mean FIM score at admission (p=0.05) and at discharge (p=0.01), and mean DRS at admission (p=0.05) were predictive of poor outcome.

Conclusions: Higher GCS scores, better scores in functional scales in hospital, less severe hyponatraemia and absence of superadded hypokalaemia predicted favourable outcome.

MeSH terms

  • Activities of Daily Living
  • Adolescent
  • Adult
  • Aged
  • Anti-Inflammatory Agents / therapeutic use
  • Brain / pathology
  • Child
  • Cohort Studies
  • Disability Evaluation
  • Disease Progression
  • Electroencephalography
  • Female
  • Glasgow Coma Scale
  • Humans
  • Hyponatremia / physiopathology
  • Magnetic Resonance Imaging
  • Male
  • Methylprednisolone / therapeutic use
  • Middle Aged
  • Myelinolysis, Central Pontine / diagnosis*
  • Myelinolysis, Central Pontine / drug therapy
  • Myelinolysis, Central Pontine / physiopathology
  • Pons / physiopathology
  • Prognosis
  • Statistics, Nonparametric
  • Treatment Outcome
  • Young Adult

Substances

  • Anti-Inflammatory Agents
  • Methylprednisolone