A girl with right heart failure related to effusive-constrictive pericarditis

Pediatr Cardiol. 2011 Jun;32(5):681-4. doi: 10.1007/s00246-011-9927-6. Epub 2011 Feb 27.

Abstract

Effusive-constrictive pericarditis is characterized by constriction of visceral pericardium with a coexisting tense pericardial effusion. We report a 10-year-old girl with right heart failure due to effusive-constrictive pericarditis. She did not present typical features, such as cardiac tamponade or thickening of pericardium (visceral and parietal), but constrictive physiology was observed by echocardiography and cardiac computed tomography. These noninvasive imaging modalities provided clinical clues to make precise diagnosis. The patient underwent surgical drainage of pericardial fluid and visceral pericardiectomy, which resulted in improved hemodynamics and symptoms.

Publication types

  • Case Reports

MeSH terms

  • Arthrogryposis / diagnosis*
  • Arthrogryposis / pathology
  • Central Venous Pressure / physiology
  • Child
  • Echocardiography*
  • Echocardiography, Doppler
  • Electrocardiography
  • Female
  • Follow-Up Studies
  • Heart Failure / diagnosis*
  • Heart Failure / pathology
  • Heart Failure / surgery
  • Hemodynamics / physiology
  • Humans
  • Pericardial Effusion / diagnosis*
  • Pericardial Effusion / pathology
  • Pericardial Effusion / surgery
  • Pericardiectomy
  • Pericarditis, Constrictive / diagnosis*
  • Pericarditis, Constrictive / pathology
  • Pericarditis, Constrictive / surgery
  • Pericardium / pathology
  • Pulmonary Wedge Pressure / physiology
  • Tomography, X-Ray Computed*
  • Ventricular Dysfunction, Right / diagnosis*
  • Ventricular Dysfunction, Right / pathology
  • Ventricular Dysfunction, Right / surgery