Purpose of review: A review of recent publications is combined with our clinical experience to provide salient tips for optimizing the care of children with congenital cholesteatoma.
Recent findings: Increasing utilization of surgical adjuncts such as endoscopy and KTP laser provides the opportunity to improve postoperative outcomes by reducing residual cholesteatoma rates and improving hearing outcomes. Nevertheless, the best prospect of leaving the child with a normal ear is achieved by prompt removal after early detection when the lesion is still small.
Summary: Education of primary care providers to promote early identification and referral of congenital cholesteatoma remains an important objective and responsibility for otolaryngologists in order to obtain optimal outcome.