Henoch-Schönlein purpura complicated by acalculous cholecystitis and intussusception, and following recurrence with appendicitis

Paediatr Int Child Health. 2016 May;36(2):157-9. doi: 10.1080/20469047.2015.1109250. Epub 2016 Jan 29.

Abstract

Henoch-Schönlein purpura (HSP) is the most common childhood systemic vasculitis. Gastro-intestinal involvement occurs in two-thirds of patients. The characteristic skin lesions generally precede abdominal symptoms or present concurrently. A 7-year-old boy presented with intussusception and acalculous cholecystitis and had a cholecystectomy. Two weeks later he was re-admitted with features typical of HSP which responded to corticosteroids. Eleven months later he presented with abdominal pain and recurrence of HSP and, at laparotomy, there was acute appendicitis. This is the first case of a child presenting with HSP complicated by acalculous cholecystitis.

Keywords: Appendicitis; Cholecystitis; Henoch–Schönlein purpura.

Publication types

  • Case Reports

MeSH terms

  • Acalculous Cholecystitis / complications*
  • Appendicitis / complications*
  • Appendicitis / surgery
  • Child
  • Cholecystectomy
  • Diagnosis, Differential
  • Glucocorticoids / therapeutic use*
  • Humans
  • IgA Vasculitis / complications*
  • IgA Vasculitis / diagnosis
  • IgA Vasculitis / drug therapy
  • Intussusception / complications*
  • Laparotomy
  • Male
  • Recurrence

Substances

  • Glucocorticoids