Calmodulin Mutants Linked to Catecholaminergic Polymorphic Ventricular Tachycardia Fail to Inhibit Human RyR2 Channels

J Am Coll Cardiol. 2017 Jul 4;70(1):115-117. doi: 10.1016/j.jacc.2017.04.055.
No abstract available

Publication types

  • Letter
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Calmodulin / genetics*
  • Heart Ventricles* / metabolism
  • Heart Ventricles* / pathology
  • Humans
  • In Vitro Techniques
  • Mutation
  • Phosphorylation
  • Polymorphic Catecholaminergic Ventricular Tachycardia
  • Ryanodine Receptor Calcium Release Channel / metabolism*
  • Tachycardia, Ventricular* / genetics

Substances

  • Calmodulin
  • Ryanodine Receptor Calcium Release Channel