A microtranslatome coordinately regulates sodium and potassium currents in the human heart

Elife. 2019 Oct 31:8:e52654. doi: 10.7554/eLife.52654.

Abstract

Catastrophic arrhythmias and sudden cardiac death can occur with even a small imbalance between inward sodium currents and outward potassium currents, but mechanisms establishing this critical balance are not understood. Here, we show that mRNA transcripts encoding INa and IKr channels (SCN5A and hERG, respectively) are associated in defined complexes during protein translation. Using biochemical, electrophysiological and single-molecule fluorescence localization approaches, we find that roughly half the hERG translational complexes contain SCN5A transcripts. Moreover, the transcripts are regulated in a way that alters functional expression of both channels at the membrane. Association and coordinate regulation of transcripts in discrete 'microtranslatomes' represents a new paradigm controlling electrical activity in heart and other excitable tissues.

Keywords: KCNH2; SCN5A; action potential; cell biology; co-knockdown; cotranslation; human; ion channels; molecular biophysics; structural biology.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • ERG1 Potassium Channel / genetics
  • ERG1 Potassium Channel / metabolism*
  • Gene Expression Regulation*
  • HEK293 Cells
  • Heart / physiology*
  • Humans
  • NAV1.5 Voltage-Gated Sodium Channel / genetics
  • NAV1.5 Voltage-Gated Sodium Channel / metabolism*
  • Potassium / metabolism*
  • Protein Biosynthesis
  • RNA, Messenger / metabolism
  • Sodium / metabolism*
  • Transfection

Substances

  • ERG1 Potassium Channel
  • KCNH2 protein, human
  • NAV1.5 Voltage-Gated Sodium Channel
  • RNA, Messenger
  • SCN5A protein, human
  • Sodium
  • Potassium