Repair of Tortuous Distal Aortic Arch Aneurysm in a 1-Year-Old Girl With PHACE Syndrome

Koji Okamoto; Yoshie Ochiai; Kunihiko Joo; Yoshiyuki Yamashita; Yusuke Nakata; Jun Muneuchi; Shigehiko Tokunaga

doi:10.1016/j.atssr.2023.02.004

Repair of Tortuous Distal Aortic Arch Aneurysm in a 1-Year-Old Girl With PHACE Syndrome

Ann Thorac Surg Short Rep. 2023 Feb 20;1(2):325-327. doi: 10.1016/j.atssr.2023.02.004. eCollection 2023 Jun.

Authors

Koji Okamoto¹, Yoshie Ochiai¹, Kunihiko Joo¹, Yoshiyuki Yamashita¹, Yusuke Nakata¹, Jun Muneuchi², Shigehiko Tokunaga¹

Affiliations

¹ Department of Cardiovascular Surgery, Japan Community Healthcare Organization (JCHO) Kyushu Hospital, Kitakyushu-city, Japan.
² Department of Pediatric Cardiology, Japan Community Healthcare Organization (JCHO) Kyushu Hospital, Kitakyushu-city, Japan.

Abstract

Herein, we describe a 21-month-old girl with PHACE syndrome (posterior fossa hemangiomas, arterial lesions, cardiac anomalies/coarctation of the aorta, and eye anomalies) who presented with a tortuous extensive aortic arch aneurysm. As the maximum short diameter of the distal aortic arch aneurysm expanded rapidly from 21 mm to 25 mm in only 5 months, we performed extensive aortic arch reconstruction with interposition graft replacement through a left thoracotomy under partial cardiopulmonary bypass.

Publication types

Case Reports