Idiopathic inflammatory myopathies (IIMs) are a heterogeneous group of autoimmune diseases characterised by skeletal muscle inflammation and frequently by other organs involvement, in particular lung and skin, but also joints, heart and gastrointestinal tract.Although they are rare diseases, the literature on IIMs has been growing rapidly and many studies have been published in order to clarify the pathogenesis and to better define diagnosis, clinical manifestations (muscular and extra-muscular) and treatment. The purpose of this review is to summarise the most relevant contributions published over the last year on this topic.