Chronic hereditary pancreatitis

Acta Gastroenterol Belg. 1994 Mar-Apr;57(2):177-80.

Abstract

Chronic hereditary pancreatitis is a rare disease accounting for 0.9% of chronic pancreatitis cases. Onset is at an earlier age than chronic alcoholic pancreatitis, often with recurrent painful episodes in childhood. We report the occurrence of hereditary pancreatitis in 3 members of a family over 3 generations.

Publication types

  • Case Reports

MeSH terms

  • Adenocarcinoma / etiology
  • Adolescent
  • Adult
  • Chronic Disease
  • Diabetes Mellitus / etiology
  • Exocrine Pancreatic Insufficiency / etiology
  • Female
  • Humans
  • Male
  • Middle Aged
  • Pancreatic Neoplasms / etiology
  • Pancreatitis / complications
  • Pancreatitis / genetics*
  • Pancreatitis / therapy
  • Pedigree